Clinical features

•May present with & without follicular mucinosis

•May be accompanied (and often is) by syringotropic MF

•Very rare & presents most commonly in middle-aged or elderly males

•Face, scalp (often associated with alopecia) & neck, trunk or limbs

•Eyebrow involvement is said to be typical

•Intensely itchy, patches, plaques or grouped papules

•Sometimes seen in tumor stage disease

•Occasionally acneiform & follicular keratosis-like lesions

•Difficult to treat because of depth of the lesions & associated with a poor prognosis

•Independent risk factor for progression

Histological features

•Epidermal involvement often absent

•Follicular infiltration by atypical lymphocytes & Sézary cells

•+/- mucinosis

•+/- syringotropic lesions

•+/- basaloid follicular hyperplasia

•Eosinophils sometimes conspicuous (eosinophilic folliculitis-like appearance)

•Granulomatous inflammation secondary to follicular destruction

•Large cell transformation occasionally present