Clinical features

•Often but not always accompanies folliculotropic mycosis fungoides

•M>F

•Wide age range (33-83, mean 58 years)

•Presents as small papules in patch or plaque stage disease, variable hair loss 

•Limbs are most affected and to a lesser extent, the head & neck & trunk

Histology may show epidermal involvement and folliculotropism. The characteristic feature is the presence of a heavy deep dermal atypical lymphocytic infiltrate surrouding and infiltrating the sweat gland & ductal epithelium. Variable numbers of Sézary cells may be present.